Dentin dysplasia type Id in a patient with chronic renal failure. A case report

Abstract

Dentin dysplasia (DD) is a rare autosomal dominant disease characterized by dentine disorganization, reduced volume of pulp chamber, pulp stones, and roots shortening. The cause of dentin dysplasia type I is still unknown; however, the cause of dentin dysplasia type II development is known, and it is associated with a defect of a gene which regulates the production of dentin sialophosphoprotein (DSPP), the major non-collagenous protein of dentin. Moreover, in extremely rare cases, dentin dysplasia might develop as a consequence of systemic diseases. Lack of the caries process and availability of calculus is explained with the laboratory parameters obtained: pH = 12.5, no cariogenic microflora found in the oral fluid, which in its turn is attributable to the fact that these microbes are unable to survive in the oral fluid with such a pH level, as well as availability of urates that have antimicrobial properties. Thus, a pediatric dentist plays an important part in diagnosing the disease, as well as such patient management and the choice of treatment methods to help them keep their teeth.